Budd-Chiari Syndrome: An Unusual Complication of Sarcoidosis
Published: 2020-09-01
Page: 160-164
Issue: 2020 - Volume 3 [Issue 2]
Raja Amri
Internal Medicine Department, Maamouri Hospital, Nabeul, Tunisia Medical University of Tunis Manar, Tunisia.
Rabie Ayari
Plastic, Hand Surgery and Burns Department, Maamouri Hospital, Nabeul, Tunisia, Medical university of Tunis Manar, Tunisia.
Mouna Medhioub
Gastroenterology Department, Maamouri Hospital, Nabeul, Tunisia Medical University of Tunis Manar, Tunisia.
Manel Loukil
Pulmonology Department, Maamouri Hospital, Nabeul, Tunisia and Medical University of Tunis Manar, Tunisia.
Haifa Tounsi
Internal Medicine Department, Maamouri Hospital, Nabeul, Tunisia Medical University of Tunis Manar, Tunisia.
Mohamed Ali Sbai
Plastic, Hand Surgery and Burns Department, Maamouri Hospital, Nabeul, Tunisia, Medical university of Tunis Manar, Tunisia.
*Author to whom correspondence should be addressed.
Abstract
Hepatic involvement during sarcoidosis is common but rarely symptomatic. Budd-Chiari syndrome is an exceptional but potentially serious complication.
A case of 38-year-old woman was diagnosed with a Budd-Chiari syndrome complicating multisystemic sarcoidosis has been reported in present case study. The patient was treated with hydroxychloroquine and long-term corticosteroid therapy with favorable clinical and radiologic outcomes.
Although BCS is an exceptional complication of hepatic sarcoidosis, it should always considered. A Doppler ultrasound should be performed in front of any evocating sign to establish an early diagnosis.
Keywords: Sarcoidosis, Budd-Chiari syndrome, cholestasis