Fascia-preserving, Less Invasive Surgery for Abdominal Wall Desmoid: A Retrospective Study of 7 Cases
Published: 2024-07-15
Page: 220-228
Issue: 2024 - Volume 7 [Issue 2]
S. N. Jatal *
Jatal Hospital and Research Centre, Latur, India.
Sudhir Jatal
Jatal Hospital and Research Centre, Latur, Tata Hospital, Mumbai, India.
Ajay Punpale
MIMSR Medical College, Latur, India.
Sachin Ingle
Department of Pathology, MIMSR Medical College, Latur, India.
*Author to whom correspondence should be addressed.
Abstract
Desmoid tumors are benign, tumors arising from connective tissue within musculoaponeurotic structures. Classically these tumors do not metastatic but locally invasive and high rate of recurrence. Desmoid tumors, also known as aggressive fibromatosis, deep fibromatosis or musculoaponeurotic fibromatosis are rare tumors. They have an incidence rate of approximately 2-4 cases per million individuals and represents about 0.03% of all neoplasms and 3% of all soft tissue tumors. The highest incidence is between the age of 30 - 40 years with a strong prevalence among fertile aged women and female to male ratio in 2:1. They are uncommon during menopause.
Desmoid tumors could be extra abdominal, intra-abdominal and abdominal wall. The commonest site is the anterior abdominal wall, with an incidence of 50% approximately 5-10% of cases are associated with familial adenomatosis polyposis and gardener syndrome.
In our study, we are reporting three female patients in between the age of 30-50 years. Diagnosis confirmed on CT imaging and wide surgical excision with clear margin was performed.
We performed Fascia-Preserving, less invasive surgery for abdominal wall desmoid.
Keywords: Desmoid tumor, desmoid fibromatosis, familial adenomatous polyposis, gardner syndrome