Asian Journal of Research in Surgery

Splenic Lymphangiomas are incredibly uncommon lesions that mostly affect children. These are divided into benign and malignant tumors, as well as real splenic cysts. A rare and slowly developing benign tumor of the spleen is called a splenic lymphangioma. So far fewer than 100 cases have been reported in the literature. The incidence of splenic lymphangioma is 80-90% in children’s less than two years age and few cases are reported in adults. Splenic lymphangiomas are accounting for less than 0.007% of all splenic tumours, that appears as a single or multiple cystic lesions of the spleen.

We report an extremely rare cases of a 38 years old male, presented with left upper quadrant abdominal pain and huge palpable lump extending up to umbilicus. We performed open total splenectomy.